Therefore, CT or MR angiography plays an important diagnostic role. However, it has its limitations as it depends on the observer capabilities and to define the exact site of interruption might be challenging. Echocardiography plays the first and important role in screening diagnosis of aortic arch anomalies which is free of radiation, particularly advantageous for paediatric population. Prior to the surgical planning, imaging plays a crucial role to know the exact types of IAA and associated cardiac anomalies. About 50% of IAA is associated with a chromosome 22q11.2 deletion (associated with DiGeorge syndrome) which is more particularly with type B. The most common anomaly is patent ductus arteriosus (PDA) which accounts for about 97% of the cases. Interrupted aortic arch is associated with intracardiac anomalies like ventricular septal defect (VSD) and patent ductus arteriosus (PDA). Type A is the second most common anomaly and is thought to result from abnormal regression of the left fourth arch segment after the left subclavian artery has ascended to its normal position. Subtype3: Isolated subcalvian artery from ductus arteriosus According to Celoria-Patton classification, IAA classified as ġ.Type A: Second most common distal to the subcalvian arterial originĢ.Type B: Most common (>50%), between the left CCA origin and subclavian arterial origin.ģ.Type C: Rare.Interruption occurs proximal to left CCA origin However, significantly decreased flow during the embryological process within the aortic arch might play an important role. It can either be complete or connected by a fibrous band. Interrupted Aortic Arch (IAA) is an uncommon congenital vascular anomaly (2-3 per million live births) where there is a separation between the ascending and descending aorta.
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